Niger J Paed 2015; 42 (1): 73 -75 | |
CASE REPORTS Dandy Walker malformation (variant): late presentation with childhood blindness |
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Ndu Ik Chinawa JM Chikani M Ibekwe R Aronu AE Edelu BO Asinobi I DOI:http://dx.doi.org/10.4314/njp.v42i1,17 Accepted: 1st October 2014 Ndu Ik Department of Paediatrics, Enugu State University Teaching Hospital Chinawa JM, Ibekwe R, Aronu AE Edelu BO, Asinobi I Department of Paediatrics, Chikani M Department of Surgery, University of Nigeria Teaching Hospital, Ituku Ozalle Enugu, Nigeria. |
Abstract: We present a rare case of Dandy Walker Syndrome in a child who presents with complaints of frontal headache, neck pain, fever, progressive visual impairment and multiple generalized tonic clonic seizures, inability to stand and urinary incontinence. Given the clinical and neuro-imaging findings, the diagnosis of Dandy Walker Variant was made. Post surgical recovery (Ventriculo peritoneal shunt) was remarkable. Unfortunately he never regained sight. The purpose of presenting this case report is to highlight the distinctive manifestation of Dandy walker syndrome to enhance early diagnosis, prompt intervention and better outcome Key words: Dandy Walker syndrome; congenital brain malformation; childhood blindness; hydrocephalus |